Table 3.

Characteristics of renal involvement at kidney biopsy and last follow-up in 13 adult patients with CFa

PatientAge (yr)bSCr (mmol/L)/GFR (ml/min per 1.73 m2)Serum Albumin (g/L)ProteinuriaHematuriaHypertensionRenal PathologyTreatmentOutcome
124107/78400.60 g/L+Exsudative GNComplete remission
220105/83441.20 g/d+FSGS calcium oxalate crystalsARBNS, CRI, ARF after PT
32764/138340.45 g/L+KWACEISCr 88 μmol/L, Pu 1.8 g/d
43171/119271.50 g/d+KWACEISCr 156 μmol/L, NS
54966/88289.50 g/dAA amyloidosisACEIESRDc
64353/116211.20 g/LMCD, CTINSpontaneous remission, PT, SCr 150 mmol/L
72374/121300.12 g/L+++IgANACEIPTc
83369/1222110.00 g/dMNACEI/ARBPT
923140/58260.15 g/LAA amyloidosisACEIPKT, SCr 60 μmol/L, Pu 0.5 g/L
102663/14236>3.00 g/LFSGSACEIc
113297/83272.20 g/L+KWLT and PT
124655/110320.60 g/dCTINPT, SCr 90 mmol/L
1337144/51231.00 g/dAA amyloidosisCRF, SCr 145 mmol/L
  • a ACEI, angiotensin-converting enzyme inhibitor; ARB angiotensin II receptor blocker; ARF, acute renal failure; CRI, chronic renal insufficiency; CRF, chronic renal failure; CTIN, chronic tubulointerstitial nephropathy; GN, glomerulonephritis; IgAN, IgA nephropathy; KW, Kimmelstiel-Wilson glomerulosclerosis; LT, liver transplantation; MCD, minimal-change disease; MN, membranous nephropathy; NS, nephrotic syndrome; PKT, pulmonary and kidney transplantation; PT, pulmonary transplantation; Pu, proteinuria; SCr, serum creatinine.

  • b Age at the time of kidney biopsy.

  • c Death.