Table 2.

Comparison of α-galactosidase activity assayed from healthy individuals in the presence and absence of GalNAc inhibitora

ParameterTotal α-Galactosidase (Assayed without Inhibitor)α-Galactosidase A (Assayed with 100 mM GalNAc)α-Galactosidase B (by subtraction)α-Galactosidase B as % of Total
Plasma (nmol/h per ml plasma; n = 20 individuals)
    observed range3.4 to 7.13.1 to 7.00.0 to 1.00.0 to 18.1
Leucocytes (nmol/h per mg protein; n = 30 individuals)
    observed range49.9 to 126.347.2 to 124.30.0 to 8.00.0 to 7.6
  • a GalNAc, N-acetylgalactosamine.