Table 5.

Incidence of ANCA-associated vasculitides with renal involvementa

Location, Country (Reference)LatitudeAnnual Incidence (per million)Population (millions)Study Period
MPAWGCSSTotal
1. Orebro, Sweden (12)59°NNDNDND16.00.20 to 0.211975 to 1995
2. Lund, Sweden (16)55°N2.5b2.1bND4.6b1.21971 to 1993
3. Norfolk, UK (7)52°N7.57.91.318.00.411992 to 1997
4. Schleswig-Holstein, Germany (8)51°N2.7c7.9c1.1c11.7c2.781988 to 2002
5. Devon, UK (25)50°NNDNDND12.40.852 yr
6. Lugo, Spain (11)43°N7.9c3.0c1.3c12.2c0.211988 to 2001
7. Miyazaki, Japan (this study)30°N14.80014.80.772000 to 2004
8. Al-Jahra, Kuwait (14)26°N20.9NDNDND0.121993 to 1996
  • a 1, 5, 7, and 8 include RLV; 2, 3, 4, and 6 may not include RLV. 1, 2, 6, and 8 are hospital-based studies; 3, 4, 5, and 7 are population-based studies. ND, not done.

  • b All cases with biopsy-proven renal involvement.

  • c ANCA-associated vasculitides without renal involvement are included.