Table 2.

General characteristics of nephropathic cystinosis patients compared with an age-matched cohort of pediatric RRT patients

Nephropathic Cystinosis Patients (n = 134)Matched Pediatric RRT Population (n = 268)
Age at start of RRT (years)10.810.7
Duration of follow-up (years)2.8 years2.8 years
Gender
    female, n (%)59 (44.0%)119 (44.0%)
    male, n (%)75 (56.0%)149 (55.6%)
RRT treatment at start
    HD, n (%)24 (17.9%)86 (32.2%)
    PD, n (%)53 (39.6%)112 (41.8%)
    Tx, n (%)47 (35.1%)46 (17.1%)
    unknown, n (%)10 (7.5%)24 (9.0%)
Last known RRT treatment (missing in 7% of control subjects)
    HD, n (%)8 (6.0%)32 (11.9%)
    PD, n (%)11 (8.2%)35 (13.1%)
    Tx, n (%)114 (85.1%)184 (68.7%)
    death, n (%)1 (0.8%)10 (3.7%)
  • All of the patients started RRT after the calendar year 1995. The patients were matched on calendar year of the start of RRT (2-year intervals) and age at the start of RRT (2-year intervals). RRT, renal replacement therapy; HD, hemodialysis; PD, peritoneal dialysis; Tx, transplantation.